| français |
-
maladie de Creutzfeldt-Jakob familiale
EXP: "fMCJ" est l'abréviation de l'anglais "familial Creutzfeldt-Jakob Disease"
Source : Manuel MSD, Professisonnels > Troubles neurologiques > Maladies à prions > Maladie de Creutzfeldt-Jakob ([Internet, 2024-12-10](https://www.msdmanuals.com/fr/professional/troubles-neurologiques/maladies-%C3%A0-prions/maladie-de-creutzfeldt-jakob))
-
synonyme :
maladie de Creutzfeldt-Jakob d'origine génétique
EXP: dans ce cas, il existe une prédisposition héréditaire à développer des prions défectueux et la maladie peut, sous cette forme, se manifester à l'âge de 50 ans déjà
Source : ScienceDirect, Revue neurologique, Phénotype inhabituel d’une maladie de Creutzfeldt-Jakob d’origine génétique, 2018 ([Internet, 2025-01-07](https://www.sciencedirect.com/science/article/abs/pii/S0035378718303278))
-
synonyme :
MCJ familiale
Source : TERMIUM Plus, "maladie de Creutzfeldt-Jakob familiale" ; Titre ([Internet, 2025-01-07](https://www.btb.termiumplus.gc.ca/tpv2alpha/alpha-fra.html?lang=fra&i=1&srchtxt=MALADIE+CREUTZFELDT-JAKOB+FAMILIALE&codom2nd_wet=1#resultrecs))
-
MCJf; fCJD abrév.
EXP: "fMCJ" est l'abréviation de l'anglais "familial Creutzfeldt-Jakob Disease"
Source : (MCJf) OFSP, Maladies > Maladies : vue d’ensemble > Maladie de Creutzfeldt-Jakob ([Internet, 2024-12-04](https://www.bag.admin.ch/bag/fr/home/krankheiten/krankheiten-im-ueberblick/cjk.html)); (fCJD) FOPH, Diseases > Diseases from A to Z > Creutzfeldt-Jakob Disease (CJD) ([Internet, 2024-12-09](https://www.bag.admin.ch/bag/en/home/krankheiten/krankheiten-im-ueberblick/cjk.html))
|
| allemand |
-
familiäre Creutzfeldt-Jakob-Krankheit
EXP: familiär vererbbare Form der Creutzfeldt-Jakob-Krankheit, die sich bereits mit 50 Jahren bemerkbar machen kann
Source : MGZ, Diagnostik > Erkrankungen > Neurogenetische Erkrankungen/Ataxie > Prion-Erkrankungen, erblich bedingt ([Internet, 2025-01-07](https://www.mgz-muenchen.de/erkrankungen/diagnose/prion-erkrankungen-erblich-bedingt.html#:~:text=Famili%C3%A4re%20Creuzfeldt%2DJakob%2DKrankheit%20%28,%2C%20progrediente%20Dysarthrie%29%20und%20Myoklonus.))
-
synonyme :
genetische Creutzfeldt-Jakob-Krankheit
Source : MeinMed.at, Krankheiten von A bis Z > Neurologie und Psychiatrie > Creutzfeldt-Jakob-Erkrankung ([Internet, 2025-01-07](https://www.meinmed.at/krankheit/creutzfeldt-jakob-krankheit/1904))
-
synonyme :
familiäre Form der Creutzfeldt-Jakob-Erkrankung
Source : nach DocCheck Flexikon, Creutzfeldt-Jakob-Erkrankung ([Internet, 2024-12-09](https://flexikon.doccheck.com/de/Creutzfeldt-Jakob-Erkrankung))
-
synonyme :
familiäre CJK
Source : MSD Manual, profi > Neurologische Krankheiten > Prionenerkrankungen > Creutzfeldt-Jakob-Krankheit (CJK) ([Internet, 2024-12-10](https://www.msdmanuals.com/de/profi/neurologische-krankheiten/prionenerkrankungen/creutzfeldt-jakob-krankheit-cjk))
-
fCJK, fCJD abrév.
EXP: familiär vererbbare Form der Creutzfeldt-Jakob-Krankheit, die sich bereits mit 50 Jahren bemerkbar machen kann
Source : (fCJK) BAG, Krankheiten > Krankheiten im Überblick > Creutzfeldt-Jakob-Krankheit ([Internet, 2024-12-04](https://www.bag.admin.ch/bag/de/home/krankheiten/krankheiten-im-ueberblick/cjk.html)); (fCJD) AT, Bundesministerium Soziales, Gesundheit, Pflege und Konsumentenschutz, Creutzfeldt-Jakob-Krankheit, 2024-07-23 ([Internet, 2024-12-04](https://www.sozialministerium.at/Themen/Gesundheit/Uebertragbare-Krankheiten/Infektionskrankheiten-A-Z/Creutzfeldt-Jakob-Krankheit.html))
|
| italien |
-
malattia di Creutzfeldt-Jakob familiare
EXP: causata da un'anomalia di uno dei due geni della proteina prionica cellulare che una persona eredita dai propri genitori; questa anomalia (mutazione) favorisce la formazione del prione nel cervello durante l'età adulta dando luogo ai sintomi della malattia, che di solito si sviluppano intorno ai 50-55 anni di età
Source : Manuale MSD, Professionisti > Malattie neurologiche > Malattie prioniche > Malattia di Creutzfeldt-Jakob ([Internet, 2024-12-10](https://www.msdmanuals.com/it/professionale/malattie-neurologiche/malattie-prioniche/malattia-di-creutzfeldt-jakob))
-
synonyme :
malattia di Creutzfeldt-Jacob genetica
Source : IT, Istituto superiore di Sanità ISS, ISSalute, Malattia di Creutzfeldt-Jacob (MCJ) ([Internet, 2025-03-12](https://www.issalute.it/index.php/la-salute-dalla-a-alla-z-menu/m/malattia-di-creutzfeldt-jacob-mcj))
-
fMCJ abrév.
EXP: causata da un'anomalia di uno dei due geni della proteina prionica cellulare che una persona eredita dai propri genitori; questa anomalia (mutazione) favorisce la formazione del prione nel cervello durante l'età adulta dando luogo ai sintomi della malattia, che di solito si sviluppano intorno ai 50-55 anni di età
Source : UFSP, Malattie > Panoramica delle malattie > Malattia di Creutzfeldt-Jakob ([Internet, 2024-12-04](https://www.bag.admin.ch/bag/it/home/krankheiten/krankheiten-im-ueberblick/cjk.html))
-
phraséologie :
forma familiare della malattia di Creutzfeldt-Jakob
Source : secondo UFSP, Malattie > Panoramica delle malattie > Malattia di Creutzfeldt-Jakob ([Internet, 2024-12-04](https://www.bag.admin.ch/bag/it/home/krankheiten/krankheiten-im-ueberblick/cjk.html))
|
| anglais |
-
familial Creutzfeldt–Jakob disease
USG: the term is usually written with "disease" in lowercase: "familial Creutzfeldt–Jakob disease"; capitalisation of "Disease" is also occasionally seen: "familial Creutzfeldt–Jakob Disease"; EXP: the tendency to develop pathogenic prions is inherited and cases of fCJD can manifest themselves from age 50 onwards
Source : Physiopedia, Prion Diseases (or Transmissible Spongiform Encephalopathies) ([Internet, 2025-07-11](https://www.physio-pedia.com/Prion_Diseases_%28or_Transmissible_Spongiform_Encephalopathies%29?et_blog&utm_source=meta&utm_medium=cpc&utm_campaign=landing-deporte&fbclid=IwZXh0bgNhZW0BMAABHXzdVJdpQDdpA3h6Nraw22tJ7EvYxGe1sFe7HVXyLGT4FQZKjWVHs0pRsA_aem_hyB9Oi23rwSlDFmWKf0ArQ&utm_id=6630696416988&utm_content=6630872179788&utm_term=6630696417388))
-
fCJD abrév.
USG: the term is usually written with "disease" in lowercase: "familial Creutzfeldt–Jakob disease"; capitalisation of "Disease" is also occasionally seen: "familial Creutzfeldt–Jakob Disease"; EXP: the tendency to develop pathogenic prions is inherited and cases of fCJD can manifest themselves from age 50 onwards
Source : Physiopedia, Prion Diseases (or Transmissible Spongiform Encephalopathies) ([Internet, 2025-07-11](https://www.physio-pedia.com/Prion_Diseases_%28or_Transmissible_Spongiform_Encephalopathies%29?et_blog&utm_source=meta&utm_medium=cpc&utm_campaign=landing-deporte&fbclid=IwZXh0bgNhZW0BMAABHXzdVJdpQDdpA3h6Nraw22tJ7EvYxGe1sFe7HVXyLGT4FQZKjWVHs0pRsA_aem_hyB9Oi23rwSlDFmWKf0ArQ&utm_id=6630696416988&utm_content=6630872179788&utm_term=6630696417388))
|
| romanche |
-
malsogna da Creutzfeldt-Jakob familiara
EXP: furma da la malsogna da Creutzfeldt-Jakob ch'è ertavla en famiglia e che po sa mussar gia en la vegliadetgna da 50 onns; "fCJD" è l'abreviaziun da l'englais "familial Creutzfeldt-Jakob Disease"
Source : Chanzlia chantunala dal Grischun, Servetsch da translaziuns, 2025
-
synonyme :
furma familiara da la malsogna da Creutzfeldt-Jakob
Source : Chanzlia chantunala dal Grischun, Servetsch da translaziuns, 2025
-
synonyme :
malsogna da Creutzfeldt-Jakob genetica
Source : Chanzlia chantunala dal Grischun, Servetsch da translaziuns, 2025
-
fCJD abrév.
EXP: furma da la malsogna da Creutzfeldt-Jakob ch'è ertavla en famiglia e che po sa mussar gia en la vegliadetgna da 50 onns; "fCJD" è l'abreviaziun da l'englais "familial Creutzfeldt-Jakob Disease"
Source : Chanzlia chantunala dal Grischun, Servetsch da translaziuns, 2025
|